occurrence of epidermolysis bullosa along with amelogenesis imperfecta in female patient of india

نویسندگان

a. p. javed

prashanth shenai

laxmikanth chatra

k. m. veena

چکیده

epidermolysis bullosa (eb) is an inherited disorder, which is characteristically presented as skin blisters developing in response to minor injury. junctional variety of eb is also associated with enamel hypoplasia. amelogenesis imperfecta presents with abnormal formation of the enamel both in deciduous and permanent dentition. this article describes a previously unreported case of amelogenesis imperfecta with complete loss of enamel in a young female patient with eb. key words: amelogenesis imperfect, epidermolysis bullosa, vesicles and bullae

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عنوان ژورنال:
dental research journal

جلد ۱۰، شماره ۶، صفحات ۰-۰

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